Search on: AMIDOHYDROLASE, ASPARTYLGLYCOSAMINE 
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Descriptor English:   Aspartylglucosylaminase 
Descriptor Spanish:   Aspartilglucosilaminasa 
Descriptor Portuguese:   Aspartilglucosilaminase 
Synonyms English:   Aspartylglucosamine Amidohydrolase
Glycosylasparaginase
Amidohydrolase, Aspartylglucosamine
Amidohydrolase, Aspartylglycosamine
Deaspartylase, Aspartylglucosylamine
Aspartylglucosaminidase
Aspartylglucosylamine Deaspartylase
Aspartylglycosamine Amidohydrolase  
Tree Number:   D08.811.277.087.125
Definition English:   An enzyme that catalyzes the conversion of N(4)-(beta-N-acetyl-D-glucosaminyl)-L-asparagine and water to N-acetyl-beta-D-glucosaminylamine and L-aspartate. It acts only on asparagine-oligosaccharides containing one amino acid, i.e. the ASPARAGINE has free alpha-amino and alpha-carboxyl groups. (From Enzyme Nomenclature, 1992) 
Entry Combination - descr/qualif English:   Aspartylglucosylaminase/deficiency use Aspartylglucosaminuria
 
History Note English:   91(75); was see under AMIDOHYDROLASES 1975-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   1234 
Unique Identifier:   D001227 

Occurrence in VHL:
 

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